DarlingRC, Disant’AgnesePA, PereraGA, AndersenDH: Electrolyte abnormalities of the sweat in fibrocystic disease of the pancreas. Am J Med Sci225: 67–70, 1953PubMed
DarlingRC, Disant’AgnesePA, PereraGA, AndersenDH: Electrolyte abnormalities of the sweat in fibrocystic disease of the pancreas. Am J Med Sci 225: 67–70, 1953PubMed)| false
Di Sant’AgnesePA, DarlingRC, PereraGA, SheaE: Sweat electrolyte disturbances associated with childhood pancreatic disease. Am J Med 15: 777–784, 1953PubMed)| false
Rendle-ShortJ; Archives Disease of Childhood: Fibrocystic disease of the pancreas presenting with acute salt depletion. Arch Dis Child31: 28–30, 1956PubMed
Rendle-ShortJ; Archives Disease of Childhood: Fibrocystic disease of the pancreas presenting with acute salt depletion. Arch Dis Child 31: 28–30, 1956PubMed)| false
TerlizziV, PadoanR, LeonettiG, VitulloP, ToscoA, TaccettiG, et al.: Cystic fibrosis and CFTR-related disorder with electrolyte imbalance at diagnosis: clinical features and outcome in an Italian cohort. Eur J Pediatr182: 5275–5283, 2023PubMed
TerlizziV, PadoanR, LeonettiG, VitulloP, ToscoA, TaccettiG, : Cystic fibrosis and CFTR-related disorder with electrolyte imbalance at diagnosis: clinical features and outcome in an Italian cohort. Eur J Pediatr 182: 5275–5283, 2023PubMed)| false
Sismanlar EyubogluT, DogruD, ÇakırE, CobanogluN, PekcanS, CinelG, et al.: Clinical features and accompanying findings of Pseudo-Bartter Syndrome in cystic fibrosis. Pediatr Pulmonol55: 2011–2016, 2020PubMed
BatesCM, BaumM, QuigleyR: Cystic fibrosis presenting with hypokalemia and metabolic alkalosis in a previously healthy adolescent. J Am Soc Nephrol8: 352–355, 1997PubMed
BatesCM, BaumM, QuigleyR: Cystic fibrosis presenting with hypokalemia and metabolic alkalosis in a previously healthy adolescent. J Am Soc Nephrol 8: 352–355, 1997PubMed)| false
SweetserLJ, DouglasJA, RihaRL, BellSC: Clinical presentation of metabolic alkalosis in an adult patient with cystic fibrosis. Respirology10: 254–256, 2005PubMed
AugustoJF, SayeghJ, MalingeMC, IllouzF, SubraJF, DucluzeauPH: Severe episodes of extra cellular dehydration: An atypical adult presentation of cystic fibrosis. Clin Nephrol69: 302–305, 2008PubMed
AugustoJF, SayeghJ, MalingeMC, IllouzF, SubraJF, DucluzeauPH: Severe episodes of extra cellular dehydration: An atypical adult presentation of cystic fibrosis. Clin Nephrol 69: 302–305, 2008PubMed)| false
Priou-GuesdonM, MalingeMC, AugustoJF, RodienP, SubraJF, BonneauD, et al.: Hypochloremia and hyponatremia as the initial presentation of cystic fibrosis in three adults. Ann Endocrinol (Paris)71: 46–50, 2010PubMed
Priou-GuesdonM, MalingeMC, AugustoJF, RodienP, SubraJF, BonneauD, : Hypochloremia and hyponatremia as the initial presentation of cystic fibrosis in three adults. Ann Endocrinol (Paris) 71: 46–50, 2010PubMed)| false
PavoneMA, Solís PadronesA, MuratoreDG, SaizM, PuigC: Hiponatremia, hipopotasemia e insuficiencia renal aguda prerrenal como presentación de fibrosis quística. [Hyponatraemia, hypopotassaemia and prerenal acute renal failure as a presentation of cystic fibrosis] Nefrologia30: 481–482, 2010PubMed
RayaCM, ZubillagaIP, SchneiderP: Alcalosis metabólica con hiponatremia, hipopotasemia e hipocloremia como forma de presentación de fibrosis quística en un adulto. [Metabolic alkalosis with hyponatremia, hypokalemia and hypochloremia as the initial presentation of cystic fibrosis in an adult patient] Med Clin (Barc)143: 137–138, 2014PubMed
RayaCM, ZubillagaIP, SchneiderP: Alcalosis metabólica con hiponatremia, hipopotasemia e hipocloremia como forma de presentación de fibrosis quística en un adulto. [Metabolic alkalosis with hyponatremia, hypokalemia and hypochloremia as the initial presentation of cystic fibrosis in an adult patient] Med Clin (Barc) 143: 137–138, 2014PubMed)| false
CaoY, DonaldsonR, LeeD: “Summer hypokalemia” as an initial presentation of cystic fibrosis in a morbidly obese African American adult: Case report. BMC Nephrol21: 462, 2020PubMed
CaoY, DonaldsonR, LeeD: “Summer hypokalemia” as an initial presentation of cystic fibrosis in a morbidly obese African American adult: Case report. BMC Nephrol 21: 462, 2020PubMed)| false
Raya CruzM, ZubillagaIP, SchneiderP: Metabolic alkalosis with hyponatremia, hypokalemia and hypochloremia as the initial presentation of cystic fibrosis in an adult patient. Med Clin (Barc)143: 137–138, 2014PubMed
Raya CruzM, ZubillagaIP, SchneiderP: Metabolic alkalosis with hyponatremia, hypokalemia and hypochloremia as the initial presentation of cystic fibrosis in an adult patient. Med Clin (Barc) 143: 137–138, 2014PubMed)| false
BergP, AndersenJF, SørensenMV, WangT, MalteH, LeipzigerJ: Alkalosis-induced hypoventilation in cystic fibrosis: The importance of efficient renal adaptation. Proc Natl Acad Sci U S A 119: e2116836119, 2022PubMed)| false
BergP, SorensenMV, RousingAQ, Vebert OlesenH, Jensen-FangelS, JeppesenM, et al.: Challenged urine bicarbonate excretion as a measure of cystic fibrosis transmembrane conductance regulator function in cystic fibrosis. Ann Intern Med175: 1543–1551, 2022PubMed
BergP, SorensenMV, RousingAQ, Vebert OlesenH, Jensen-FangelS, JeppesenM, : Challenged urine bicarbonate excretion as a measure of cystic fibrosis transmembrane conductance regulator function in cystic fibrosis. Ann Intern Med 175: 1543–1551, 2022PubMed)| false
BergP, JensenT, AndersenJF, SvendsenSL, ModvigIM, WangT, et al.: Loss of the secretin receptor impairs renal bicarbonate excretion and aggravates metabolic alkalosis in mice during acute base-loading. J Am Soc Nephrol34: 1329–1342, 2023PubMed
BergP, JensenT, AndersenJF, SvendsenSL, ModvigIM, WangT, : Loss of the secretin receptor impairs renal bicarbonate excretion and aggravates metabolic alkalosis in mice during acute base-loading. J Am Soc Nephrol 34: 1329–1342, 2023PubMed)| false
WallSM: Regulation of blood pressure and salt balance by pendrin-positive intercalated cells: Donald Seldin Lecture 2020. Hypertension79: 706–716, 2022PubMed
WallSM: Regulation of blood pressure and salt balance by pendrin-positive intercalated cells: Donald Seldin Lecture 2020. Hypertension 79: 706–716, 2022PubMed)| false
Varasteh KiaM, BaroneS, McDonoughAA, ZahediK, XuJ, SoleimaniM: Downregulation of the Cl−/HCO3−exchanger pendrin in kidneys of mice with cystic fibrosis: Role in the pathogenesis of metabolic alkalosis. Cell Physiol Biochem45: 1551–1565, 2018PubMed
Varasteh KiaM, BaroneS, McDonoughAA, ZahediK, XuJ, SoleimaniM: Downregulation of the Cl−/HCO3−exchanger pendrin in kidneys of mice with cystic fibrosis: Role in the pathogenesis of metabolic alkalosis. Cell Physiol Biochem 45: 1551–1565, 2018PubMed)| false
ProcinoG, MilanoS, CarmosinoM, BarbieriC, NicolettiMC, LiJH, et al.: Combination of secretin and fluvastatin ameliorates the polyuria associated with X-linked nephrogenic diabetes insipidus in mice. Kidney Int86: 127–138, 2014PubMed
ProcinoG, MilanoS, CarmosinoM, BarbieriC, NicolettiMC, LiJH, : Combination of secretin and fluvastatin ameliorates the polyuria associated with X-linked nephrogenic diabetes insipidus in mice. Kidney Int 86: 127–138, 2014PubMed)| false
AzroyanA, MorlaL, CrambertG, LaghmaniK, RamakrishnanS, EdwardsA, et al.: Regulation of pendrin by cAMP: Possible involvement in β-adrenergic-dependent NaCl retention. Am J Physiol Renal Physiol302: F1180–F1187, 2012PubMed
DevlinJ, BeckettNS, DavidTJ. Elevated sweat potassium, hyperaldosteronism and pseudo-Bartter's syndrome: a spectrum of disorders associated with cystic fibrosis. J R Soc Med82: 38–43, 1989PubMed
DevlinJ, BeckettNS, DavidTJ. Elevated sweat potassium, hyperaldosteronism and pseudo-Bartter's syndrome: a spectrum of disorders associated with cystic fibrosis. J R Soc Med 82: 38–43, 1989PubMed)| false
PedroliG, Liechti-GallatiS, MauriS, BirrerP, KraemerR, Foletti-JäggiC, et al.: Chronic metabolic alkalosis: not uncommon in young children with severe cystic fibrosis. Am J Nephrol15: 245–250, 1995PubMed
PedroliG, Liechti-GallatiS, MauriS, BirrerP, KraemerR, Foletti-JäggiC, : Chronic metabolic alkalosis: not uncommon in young children with severe cystic fibrosis. Am J Nephrol 15: 245–250, 1995PubMed)| false
SpoletiniG, FitchG, GillgrassL, EtheringtonC, CliftonI, PeckhamDG: Urinary bicarbonate and metabolic alkalosis during exacerbations in cystic fibrosis. ERJ Open Res 8: 00669–02021, 2022PubMed)| false